Before eculizumab therapy After eculizumab therapy P value
Gender, n (%) /
Male 1 (20%) 1 (20%)
Female 4 (80%) 4 (80%)
Median age (range) (year) 59 (26, 67) 59 (26, 67) /
Classification, n (%) /
Classical 3 (60%) 3 (60%)
Combined with BMD 2 (40%) 2 (40%)
Subclinical 0 (0%) 0 (0%)
WBC (×109/L) (range) 2.85 (2.27, 10.54) 3.09 (2.1, 5.64) 0.504
ANC (×109/L) (range) 2.24 (0.74, 9.35) 1.79 (0.17, 4.62) 0.686
RBC (×1012/L) (range) 1.96 (1.32, 2.47) 2.45 (2.24, 2.66) 0.01
Hb (g/L) (range) 64 (43, 80) 83 (67, 87) 0.005
BPC (×109/L) (range) 74 (50, 306) 81 (38, 319) 0.448
LDH (U/L) (range) 3667 (1075.1, 4887) 915 (460, 1822) 0.028
GFR (ml/min/1.73m2) (range) 84.47 (36.31, 130.54) 85.53 (42.25, 129) 0.742
IBIL (μmol/L) (range) 31.71 (14.7, 83.5) 20.69 (4.3, 24.1) 0.057