Conclusion
Adams-Oliver syndrome remains a complex, rare congenital disorder, with very little documented in the scientific literature. It is essentially autosomal dominant, but recessive and sporadic modes have also been reported. This multisystem pathology, requiring regular follow-up, affects the quality of life and can be fatal if internal organs are affected. This syndrome requires a continuous and comprehensive multidisciplinary approach, from birth until the best medical, social, and psychological conditions are obtained.