LQTS-Long QT syndrome, SCD-Sudden cardiac death, TDP-Torsade’s de
pointes, TWA-T wave alternans. QTc interval ≥ 480 ms:
31. Score ≥ 3.5 indicates high probability of Long QT
syndrome.
Table 2: Probabilistic score based on Modified Schwartz’s
criteria2.
Case.4:
A 2 year 8-month-old boy, 3rd in birth order with
uneventful antenatal and immediate post-natal period presented with
recurrent episodes of syncopal attacks and an episode of
unresponsiveness with successful resuscitation. He had congenital
bilateral sensorineural hearing loss and underwent cochlear
implantation. Father and two older siblings have prolonged QTc
interval (> 450 ms). He was diagnosed to have long QT
syndrome and underwent LCSD and implantable loop recorder through left
posterolateral thoracotomy.