LQTS-Long QT syndrome, SCD-Sudden cardiac death, TDP-Torsade’s de pointes, TWA-T wave alternans. QTc interval ≥ 480 ms: 31. Score ≥ 3.5 indicates high probability of Long QT syndrome.
Table 2: Probabilistic score based on Modified Schwartz’s criteria2.
Case.4:
A 2 year 8-month-old boy, 3rd in birth order with uneventful antenatal and immediate post-natal period presented with recurrent episodes of syncopal attacks and an episode of unresponsiveness with successful resuscitation. He had congenital bilateral sensorineural hearing loss and underwent cochlear implantation. Father and two older siblings have prolonged QTc interval (> 450 ms). He was diagnosed to have long QT syndrome and underwent LCSD and implantable loop recorder through left posterolateral thoracotomy.