10y, M |
Redness and loss of vision OD, papilloedema OS |
Brain
CT scan: Midline Intraventricular tumour involving lateral ventricle |
Intracranial, intraventricular glioma |
Had Neurosurgical excision,
Histology showed pleomorphic xanthoathrocytoma
27(rare) |
14y, M |
Upper lid mass OS, Poor school performance |
Orbitocranial CT scan: Orbital mass extending to middle cranial
fossa with erosion of medial & posterior walls of orbit and expansion
of sella |
Malignant optic nerve glioma |
Multidisciplinary team surgery
recommended, not done |
15y, F |
Cranio-facial mass with intracranial extension, OS |
Orbitocrainal CT scan: Hyperdense orbito-cranial tumour
extending from left middle cranial fossa, containing intralesional
calcifications with absence of lesser wing sphenoid (Sphenoid aplasia) |
Optic nerve glioma with sphenoid aplasia and orbital plexiform
neurofibroma |
Multidisciplinary team surgery recommended, not
done |
17y, M |
Poor vision x 10 years, Poor school performance, Optic atrophy
OU, Mother had cutaneous NF nodules |
Brain MRI: Well-defined
mass involving tuber-cenerum and optic chiasm extending to optic tracts
OU; Worse on left |
Hypothalamic-optic pathway glioma |
Multi-disciplinary team care required, not available |
18m, M |
Upper back mass with scoliosis |
MRI spine: Scoliosis |
Plexiform neurofibroma upper back with scoliosis |
Multi-disciplinary
team care required, not available |
7y, M |
Right sided cranio-facial mass since birth, short stature |
Orbito-cranial MRI: right soft tissue facial mass, some diffuse
signal changes in cerebellum |
CNS Harmatoma and craniofacial
neurofibroma |
Had oculoplastic debulking surgery awaiting
reconstruction |