INTRODUCTION
Levoatrial cardinal vein (LACV) is an abnormal connection between the left atrium or pulmonary veins and any systemic vein which is derived from cardinal venous system (1). Most often, this anomaly has been described in the context of left‑sided obstructive cardiac lesions such as mitral atresia or hypoplastic left heart (2). It has been reported to be seen together with left heart pathologies and additionally anomalies such as double –outlet right ventricle, tetralogy of Fallot (3), ventricular septal defect and atrioventricular septal defect. Presence of the levoatrial cardinal vein without a cardiac anomaly is a very rare congenital anomaly of the systemic venous return.
In the literature, no LACV anomaly was found in two siblings who were asymptomatic and did not have an additional cardiac anomaly. Therefore, we present two cases ( two siblings ) the echocardiographic finding, computed tomography (CT) and aniographic images who were diagnosed with levoatrial cardinal vein and did not have any additional cardiac pathology. At the same time, we wanted to share the information that genetic tests are planned due to this rare anomaly in two siblings.