ACA, anti centromere antibody; RNAPIII, RNA polymerase III; lcSSc,
limited cutaneous systemic sclerosis; mRSS, modified Rodnan skin score;
PAH, pulmonary arterial hypertension; ILD, interstitial lung disease;
GIS, gastrointestinal system; DU, digital ulcer; SRC, scleroderma renal
crisis; ANA, antinuclear antibody
Table 4. Clinical features of the patients who were positive
only for uncommon scleroderma-specific autoantibodies