Scl 70 (N=41) Scl 70 (N=41) Scl 70 (N=41) ACA (N=27) ACA (N=27) ACA (N=27) RNAPIII (N=15) RNAPIII (N=15) RNAPIII (N=15)
Single n=28 Multiple n=13
p
Single n=16 Multiple n=11
p
Single n=6 Multiple n=9
p
lcSSc 9 (32.1%) 6 (46.2%) 0.386 16 (100%) 11 (100%) NA 2 (33.3%) 3 (33.3%) 1.000
Female 27 (96.4%) 11 (84.6%) 0.176 15 (93.8%) 11 (100%) 1.000 4 (66.7%) 7 (77.8) 0.634
ILD 17 (60.7%) 7 (53.8%) 0.678 0 1 (9.1%) 0.407 4 (66.7%) 5 (55.6) 0.667
PAH 1 (3.6%) 0 0.490 0 0 NA 1 (16.7%) 1 (11.1%) 0.756
Malignancy 0 0 NA 0 0 NA 2 (33.3%) 0 0.143
DU 2 (7.1%) 2 (15.1%) 0.579 0 4 (36.4%) 0.019 1 (16.7%) 1 (11.1%) 0.756
GIS 15 (53.6%) 9 (69.2%) 0.499 8 (50%) 7 (63.6%) 0.696 4 (66.7%) 7 (77.8%) 0.634
Overlap 4 (14.3%) 1 (7.7%) 1.000 7 (43.8%) 4 (36.4%) 0.508 0 1 (11.1%) 1.000
Age 47.9±12.9 44.8±12.6 0.792 51.5±10.2 48.9±10.7 1.000 60.2±9.9 52.1±5.9 0.088
Disease duration 2±1.5 2.1±1.5 0.810 1.9±1.1 2.1±1.8 0.809 3±1.3 2.3±1.8 0.328
mRSS 13.9±9.3 15.2±15.5 0.690 6.6±5.4 6.3±5.1 0.942 14.5±12.6 24.3±13.9 0.145