Abstract
Here we report a case of a previously unoperated 35-year-old male TOF
patient. He was admitted due to dyspnea, initial physical examination
demonstrated cyanosis and heart murmurs. Echocardiography suggested
secundum atrial septal defect, perimembranous ventricular septal defect
and mild-severe aortic regurgitation. Computed tomography angiography
indicated aortic root dilation and suspicious right coronary artery
aneurysm. Concurrent repair of TOF and VSARR was performed successfully
and the patient had a satisfactory recovery.
Enlargement of the aorta is a severe sequela of tetralogy of Fallot
(TOF), which can lead to fatal outcomes like aortic regurgitation (AR),
dissection, aneurysm, or even rupture with fatal consequences, even in
those patients who have had a repair of TOF.[1] Valve sparing aortic
root replacement (VSARR), also known as the Yacoub technique, is a
surgical procedure that has the advantages of correcting AR, preserving
native aortic valves, avoiding prosthetic valves and subsequent
requirement for long-term anticoagulation treatment.[2] Several
studies have demonstrated the effectiveness of VSARR in patients with AR
complicated by aortic root dilation following a repair of congenital
heart defects.[2, 3] To date, VSARR has not been performed on TOF
patients undergone no intervention. Here we described a case of a
previously unoperated TOF patient undergoing VSARR and concurrent repair
of TOF successfully.