Persistent left superior vena cava draining into the left atrium is a
rare condition. We herein report the case of a 34-year-old male admitted
at our institution for paroxysmal atrial fibrillation. Investigations
revealed a large ostium secundum atrial septal defect, with a persistent
left superior vena cava draining into the left atrium, while the
coronary veins drained separately into the left atrium. Surgical
correction was performed, closing the defect with a patch and connecting
the left superior vena cava to the right atrial appendage with an
extra-cardiac conduit.