Introduction
Neurolymphomatosis is a rare clinical entity in which lymphoma cells with neurotropism infiltrate and destroy peripheral nerves, spinal nerve roots, nerve plexuses and cranial nerves. [1,2,3] Neurolymphomatosis associated with T cell lymphoma is very rare.[1] In large series, T cell lymphoma was diagnosed in 2.5-10 % of neurolymphomatosis cases [1,2,3]. We hereby report a very unusual case of CNS involvement by ALCL with bilateral optic neurolymphomatosis resulting in permanent blindness.