Conclusion
Congenital heart disease with LSVC should be aware of the presence of
UCSS. Preoperative TTE is still the main method to diagnose UCSS, and it
can improve the diagnostic rate of TTE to strengthen the understanding
of the pathologic anatomy and pathophysiological characteristics of this
cardiac malformations. According to the location of LSVC into the LA,
different surgical methods were selected, and satisfactory results were
achieved. The mortality rate of this series of patients was 3.1%
(5/159), the cause of death mainly depends on the complexity and
severity of the associated cardiac malformations.