Conclusion:
Truncus arteriosus is infrequent congenital heart disease with
mortality comparable to that following Norwood procedure. Mortality
rates have trended down over time although continue to remain high.
22q11.2 deletion was not associated with increased mortality compared to
subjects without this deletion. However, this subject population had a higher incidence of non-cardiac anomalies, higher need for tracheostomy
and G-tube placement, protracted length of stay with an increased cost of
hospitalization. Prematurity, non-White race, and use of Medicaid
insurance were factors associated with higher mortality. These findings
will help direct prenatal counseling and management postnatally.