Introduction
Superior vena cava stenosis is an uncommon anomaly, usually seen as postoperative complication following cardiac surgery.1, 2 True congenital SVC stenosis is even rarer and can be lethal, if not addressed in time. Rapid resolution of symptoms is possible by stent angioplasty.3 Association with obstructed TAPVC can lead to pulmonary venous hypertension, along with SVC syndrome. Physical findings should prompt detailed and focused evaluation for timely intervention. To the best of our knowledge, congenital SVC stenosis in association with obstructed supracardiac total anomalous pulmonary venous connection (TAPVC) has never been reported